Invitrogen

GNS Polyclonal Antibody

产品信息

PA5-47329

应用

建议稀释比

已发表文章

免疫印迹 (WB)

0.1 µg/mL

免疫沉淀 (IP)

25 µg/mL

产品规格

种属反应

Human

宿主/亚型

Goat / IgG

分类

Polyclonal

类型

Antibody

抗原

Mouse myeloma cell line NS0-derived recombinant human Glucosamine (N-acetyl)-6-Sulfatase/GNS Val37-Leu552

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偶联物

Unconjugated Unconjugated Unconjugated

形式

Lyophilized

浓度

0.2 mg/mL

纯化类型

Antigen affinity chromatography

保存液

PBS with 5% trehalose

内含物

No Preservative

保存条件

-20° C, Avoid Freeze/Thaw Cycles

运输条件

Ambient (domestic); Wet ice (international)

RRID

AB_2609386

产品详细信息

Reconstitute at 0.2 mg/mL in sterile PBS.

靶标信息

GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.

仅用于科研。不用于诊断过程。未经明确授权不得转售。