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产品信息
MA5-50387
产品规格
种属反应
Human,
Mouse,
Rat
宿主/亚型
Rabbit
/ IgG
Expression System
HEK293 cells
分类
Recombinant Monoclonal
类型
Antibody
克隆号
HL2122
抗原
Recombinant fragment of human OTC.
偶联物
形式
Liquid
浓度
1 mg/mL
纯化类型
Protein A
保存液
PBS
内含物
no preservative
保存条件
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
运输条件
Wet ice
RRID
AB_3094281
靶标信息
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
仅用于科研。不用于诊断过程。未经明确授权不得转售。
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生物信息学
蛋白别名: Ornithine carbamoyltransferase, mitochondrial; ornithine transcarbamylase; Ornithine transcarbamylase, mitochondrial; OTCase; sparse fur
基因别名: AI265390; OCTD; OTC; Sf; spf
UniProt ID: (Human) P00480, (Mouse) P11725, (Rat) P00481
Entrez Gene ID: (Human) 5009, (Mouse) 18416, (Rat) 25611
urea cycle
liver development
ornithine catabolic process
midgut development
response to zinc ion
citrulline biosynthetic process
response to insulin
arginine biosynthetic process via ornithine
response to drug
anion homeostasis
protein homotrimerization
response to biotin
ammonia homeostasis
cellular amino acid metabolic process
arginine biosynthetic process
ornithine metabolic process
cellular amino acid biosynthetic process
response to nutrient levels
